ABNORMALITIES IN DERMAL CONNECTIVE TISSUE. Erik Austin, D.O., M.P.H. Elastosis perforans serpiginosa – Serpiginous arrangement of confluent, keratotic papules on the arms, face/neck, legs. Keratotic papules of EPS Typical site affected = neck. Elastosis perforans serpiginosa EPS.
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ABNORMALITIES INDERMAL CONNECTIVE TISSUE
Erik Austin, D.O., M.P.H.
Hyperelastic epidermis that clutches the increased dermal elastic fibers like a claw
Transepidermal elimination of neutrophils and elastic fibers from the dermis through a channel in the epidermis
Inborn error in the metabolism if methionine
ERRORS IN METABOLISM
Periorbital ecchymosis, “raccoon sign”
Extremities, trunk, genitals and face with localized nodules
Congenital erythropoietic porphyria (CEP)
Erythropoietic protoporphyria (EPP)
Erythropoietic coproporphyria ECP
Acute intermittent porphyria (AIP)
ALA dehydrogenase deficiency
Hereditary coproporphyria (HCP)
Variegate porphyria (VP)
Porphyria cutanea tarda
Multiple erosions with hemorrhagic crusts, as well as an intact blister on the lateral fourth finger
sunbed use, hemodialysis
Fluorescence of circulating red blood cells, CEP with UVA
Vs. transient fluorescence in EPP