E N D
NEONATOLOGY CASE HISTORY VNMU SHIWANAND Gope 90A Ebiringha chinaekpera sandra 90A Shigwedha hileni N.n
HISTORY • RH –ve WOMEN WITH 2ND PREGNANCY • PREVIOUS BABY WAS NORMAL BUT Rh+VE • IT WAS A TERMED CHILD FULLY MATURED WITH GESTSTIONAL AGE 40 WEEKS AND IT WAS A NORMAL DELIVERY. • PREGNANCY ULTRASOUD WAS NORMAL.
ANAMNESIS OF NEW BORN • BODY WEIGHT- 3KG • LENGTH- 57CM • AGE- 2 DAYS OLD • APGAR SCORE- 09 • ICTERUS APPEARED 1ST DAY OF LIFE AND ANEMIA.
DIAGNOSIS • HEMOLYTIC DISEASE OF NEWBORN, RH INCOMPATIBILITY ICTERIC ANEMIC FORM, MODERATE GRADE.
STATUS LOCALIS • DAY 1- • TEMPERATURE- 37DEGREE • BR- 43\MIN • HR- 153\MIN • ICTERUS OF HEAD AND TRUNK • LIVER AND SPLEEN SLIGHTLY ENLARGED
STATUS LOCALIS • DAY 2- • TEMPERATURE – 37 DEGREE C • BR- 42 PER MIN • HR- 153 PER MIN • ICTERUS OF HEAD, TRUNK AND EXTREMITIES EXCEPT FOR FEET AND PALM • ANEMIA • STOOL AND URINE IS NORMAL
CLINICAL FORM PRESENT • JAUNDICE • ANEMIA
CLINICAL PRESENTATION SHOWING ANEMIA • PALLOR SKIN • LESS INTENSIVE JAUNDICE • MILD HEPATOSPLENOMEGALY ON ULTRASOUND
CLINICAL PRESENTATION SHOWING JAUNDICE • ICTERIC AMNIOTIC FLUID • VERNIX CASEOSA AND UMBLICAL CORD • INTENSIVE JAUNDICE THAT APPEARS WITHIN FIRST 24 HOURS • 3 KARMER'S ZONE • LETHARGY DUE TO BILIRUBIN ENCEPHALOPATHY
EVALUATION OF JAUNDICE • CLINICAL EXAMINATION SHOWS COLOUR OF SKIN AFTER SLIGHT PRESSING WITH THE FINGER TO THE DEPTH OF THE SUBCUTENEOUS FAT. • ACCORDING TO MODIFIED KRAMER'S SCALE SCORE IS 4 AS ICTERUS OF HEAD TRUNK AND EXTREMITIES EXCEPT FOR PALM AND FEET. • SO ESTIMATED SERUM BILLIRUBIN LEVEL 250mcM/L
LAB DIAGNOSTICS • ANEMIA • HYPERBILIRUBINEMIA {CORD BLOOD BILLIRUBIN MORE THAN 4mg\dL • PREVALANCE OF INDIRECT BILIRUBIN [NORMAL STOOL AND URINE COLOUR] • RETICULOCYTOSIS [30%] • BLOOD GROUP INCOMPATIBILITY • HYPOALBUMINEMIA • SMEAR SHOWS... POLYCHROMASIA, ANISOCYTOSIS, NO SPHEROCYTES.
TREATMENT PRINCIPLES • PHOTOTHERAPY • MEDICATIONS • EXCHANGE TRANSFUSION • ADEQUATE HYDRATION AND FEEDING • PREVENTION OF COMPLICATIONS • ANTENATAL PROPHYLAXIS
PHOTOTHERAPY • BABY WAS PLACED IN A SUPINE POSITION AFTER FEEDING. • THE BABY WAS UNDRESSED TO MAXIMISE THE AREA OF TREATMENT. • BABY WAS PROVIDED LIGHT PROOF PROTECTION TO PROTECT THE EYES • THE TEMPERATURE WAS CONTINUOUSLY MONITORED • CONTINUED WEIGHTTAKING WAS DONE TO SEE BABYS CONDITION AND STATE OF HYDRATION • FIBREOPTIC PHOTOTHERAPYBLANKETS WHERE USED. • CONTINUOUS PHOTOTHERAPY UP TO 16 –18 HRS WASPROVIDED EVERY DAY FOR 5 DAYS.
STOPPING PHOTOTHERAPY • THE PHOTOTHERAPY WAS STOPPED AFTER THE SERUM BILIRUBIN HAS FALLEN TO 50mcmol\L
FEEDING • ENTERNAL FEEDING • CONTINUE LACTATION AND FEEDING SUPPORTS • MATERNAL EXPRESSED MILK WHEN ADDITIONAL FEEDS ARE INDICATED