Left Ventricular Hypertrabeculation (LVHT)/Left Ventricular Non-Compaction (LVNC): An Unclassified Form of Cardiomyopathy. Lorna Estabrooks , RN, MN,CCN(C), CNCC(C), Paula Price , RN, PhD . Susan Beischel , RN, MN .
Left Ventricular Hypertrabeculation (LVHT)/Left Ventricular Non-Compaction (LVNC):
An Unclassified Form of Cardiomyopathy.
Lorna Estabrooks, RN, MN,CCN(C), CNCC(C),Paula Price, RN, PhD. Susan Beischel, RN, MN.
Department of Advanced Specialty Health, Mount Royal College, Calgary, Alberta, Canada.
(1) extensive spongy transformation of the LV myocardium and frequently associated with other cardiac morphologic abnormalities;
(2) prominent coarse trabeculations of the ventricular wall and deep recesses of the ventricular cavity;
(3) a dysplastic appearance of the myocardium with thinned myocardium and excessive trabeculations.
(2) it might result from an attempt of an impaired myocardium to grow and, thus, trying to overcome an inborn error so the trabeculations in the ventricles enable the myocardium to increase its mass (Sedmera, Pexieder, Vuillemin, Thompson, & Anderson, 2000),
(3) it might be the result of an adaptation to special hemodynamic conditions (Agnisola & Tota, 1994),
(4) it might be the consequence of an impaired adhesion of cardiac myocytes as a result of malfunction of gap junctions (Spach, 1994),
(5) it might be a result of a cardiac neuropathy, a disturbance associated with the cardiac conduction system comprising His- and Purkinje fibres (Ansari & Ho, 1999).
Monitor for signs and symptoms of heart failure, tachyarrhythmias, and emboli.
Patient and family counseling and education related to LVNC/LVHT being genetic and heterogeneous.
Patients maybe asymptomatic.
Awareness that prevalence is higher than previously thought & prevalence has increased with the improvement of cardiac imaging (echocardiography & cardiac MRI and CT).
(Towbin & Bowles, 2002)